Neurofibromas are slow growing, benign tumours of peripheral nerve tissue seen frequently in association with neurofibromatosis type 1. Although the third decade of life is when presentations are at their peak, cases have been documented in people as young as 10 months to as old as age of 70. The true nature of the disease is often revealed by histopathological evaluation. The isolated occurrence of neurofibroma in maxillary sinus is rare with less than 10 cases reported in literature. Here, we report a rare case of solitary neurofibroma of left maxillary sinus without generalised syndrome of neurofibromatosis in a 27-year-old female patient.