Solid pseudopapillary epithelial neoplasm (SPEN) of the pancreas are exceptional cystic exocrine tumour of the pancreas with low incidence rate. It is most prevalent in young women between 30 and 40 years of age [1]. It is also known as a Frantz or Hamoudi tumour. SPEN has very low-grade malignant potential, with only 5% of patients developing metastases but it is more aggressive and locally invasive in men. Early detection of this tumour of this tumour is important as , it usually has a good prognosis following surgical resection but poor prognosis factors are male sex, vascular or local invasion, size >5 cm, and necrosis or cellular atypia[2] . SPEN can present similar to other pancreatic tumours. This case report aims to describe the clinical and pathological findings in a patient diagnosed with SPEN and present the treatment and its outcome.