Annotation. Rhabdomyoma of the heart refers to benign neoplasm, often diagnosed in the first year of life, can cause serious disorders in the work of the heart. In some cases, rhabdomyoma of the heart is observed with tuberoussclerosis e, in this regard, it is necessary to conduct a full examination of the child and promptly prescribe treatment and regular monitoring.Early detectionof rhabdomyoma of the heart and дprenatal observation of a cardiologist and cardiac surgeon with symptomatic treatment will allow you to choose the right treatment strategy, since in some cases there isa regression of rhabdomyoma.