Abstract Background: Hydatid disease is a zoonosis caused by Echinococcus tapeworms. Hydatid disease has wide geographic distribution and is considered a public health problem in developing country. Objective: The present study was carried out to evaluate the demographic characteristics, clinical presentations, and management of the patients of the hydatid disease Material & Method: The current study is a retrospective study for the patients attending a tertiary care hospital Rajasthan between august 2017 to august 2022. The information was gathered from medical records. Data was entered in Microsoft Excel and used SPSS version 22 Results: 36 diagnosed patients of hydatid disease underwent during the study period, 72.2% of them were males and half of the patients were > 40 years of age. 69.4% residing at rural areas and 47.2% was belonged to lower socio-economic class. Liver was the most common site (80.5%) of involvement. Abdominal pain (94.4%) followed by nausea/vomiting (47.2%), was the most common complaint, whereas abdominal mass (58.3%) followed by palpable liver (33.3%) were the most common physical finding in our study population. Cystobilliary fistula was the common post-operative complication in hydatid disease. Surgery was the treatment of choice. Conclusion: In hydatid disease liver was the main organ involved, abdominal pain and lump were main presenting complaints. Open surgery was the mainstay of treatment.