Abstract: Congenital malformations of the ureters, in particular the megaureter, are a frequent and reasonably common pathology of the urinary system. According to different authors, it makes up from 22% to 40% of all malformations. The increase in the number of early diagnosis of this disease, the lack of a unified view of the factors of their development, the use of various diagnostic methods, the presence of a large number of surgical treatment methods, the high percentage of unsatisfactory results and the prospect of developing new treatment algorithms make this disease an urgent issue of pediatric surgery.