Intradural extramedullary arachnoid cyst in the spine is extremely uncommon, with only 5% occurring in this site. These cysts rarely cause compression of the spinal cord. The etiology of these cysts is uncertain, however, the majority are congenital. Other possible causes include - trauma, infection, inflammation, postoperative complication, or lumbar puncture. Diagnosis can be establishedusing MRI. If the patient is asymptomatic, conservative therapy is advised. Complete excision isrecommended for patients with clinical symptoms and severe neurological damage.