Nuclear protein in Testis (NUT) Midline carcinoma (NMC) is highly aggressive, lethal, uncommonly encountered variant of squamous cell carcinoma, caused by genetic re-arrangement of NUT gene with a gene from BRD family1 . 143 patients were registered to International NMC Registry between 1990 to 20172 .Similarly data of 119 patients from 64 literatures published between 1950 to 2017 were retrieved on PUBMED and Google search3 . Diagnosis of NMC has increased annually since 20074, 10 (Figure 1).Median age of onset is 24 years1with equal incidence in male and female.2Most common site of occurrence is thoracic (54%) followed by Head and Neck. (40%) 2 Among Head and Neck NMC sinonasal origin is commonest.1,2,3,5,6,11.Median Overall Survival quoted by various literatures is about 6.8 months2 .We report a case of a boy who presented to us with typical features of NM