• CCAM (congenital cystic adenomatoid malformation) is a rare pulmonary developmental hamartomatous defect that involves one or more lobes of the lung and is made up of pulmonary tissue with aberrant bronchial growth. This is a case report of a newborn who underwent surgical excision of CCAM at the age of 20 days. The neonate had CCAM TYPE 1 in the right lower lobe but no cardiac involvement. The surgical procedure called for mild supported manual ventilation until the thorax was opened, then regulated ventilation with judicious fluid management, intra-operative care of hypercarbia and hypoxia, and meticulous post-operative surveillance. With satisfactory respiratory function, surgical excision of the cyst and lobe was successful. Introduction